Guillermo Quintero VegaDaniel OsorioJosé De La HozKaren GalvisRafael AndradeDaniela Rodríguez2026-03-222026-03-22202010.22541/au.159534196.65498395https://doi.org/10.22541/au.159534196.65498395https://andeanlibrary.org/handle/123456789/84075IgG4-related disease (IgG4-RD) is a chronic inflammatory mediated by an immune response characterized by dense lymphoplasmacytic infiltrate, IgG4 positive plasmocytes in the affected tissue. In this case, we describe a patient who presented pericarditis with hemodynamic instability. Reporting of atypical presentations is necessary for broadening clinical recognition of similar cases.enPericarditisMedicineDiseasePathologyCardiologyIgG4-related disease manifesting as pericarditis: A case report and Literature Reviewpreprint