Mesenteric polycystic lymphangiomatosis in a pediatric patient. Case report

Abstract

Introduction: Mesenteric polycystic lymphangiomas are rare cystic tumors, with a 5% incidence compared to their incidence in the neck and axillae (95%), seen more frequently in pediatric patients, rare in patients over 20 years of age.Clinical case: A 3-year-old male patient presents with a clinical picture of one day of evolution, reporting abdominal pain of moderate intensity, temperature rises and vomiting. Physical findings show abdominal distension, with ultrasound showing a polycystic lesion, and contrast-enhanced tomography corroborating a lobulated multi-separated cystic formation. Exploratory laparotomy revealed a polycystic tumor at the level of the ileum mesentery. The anatomopathological study describes a polycystic mesenteric lesion. Exeresis is performed and the postoperative evolution is satisfactory.Conclusions: Polycystic mesenteric lymphangiomatosis is a rare tumor that mainly affects the mesentery of the small intestine and/or colon. In pediatric age, this condition should be considered as a differential diagnosis of acute abdomen. Conventional or laparoscopic surgery is the cornerstone of treatment